以锥体外系为主要临床表现的渗透性脱髓鞘综合征1例One case of osmotic demyelination syndrome with extrapyramidal system as the main clinical manifestation
郑雪姣,高晓宇,狄政莉,景芸芸,燕玉娥
摘要(Abstract)：
目的总结渗透性脱髓鞘的临床特点、影像学特点及治疗方法。方法回顾性分析以椎体外系为表现渗透性脱髓鞘患者的临床特点、诊治过程、随访与文献复习。结果患者主要表现为椎体外系症状,在发病过程中电解质始终正常,未出现低钠血症。头颅MRI示,脑桥中央和基底节区T_2加权高信号,T_1加权低信号,头颅DWI呈高信号。经甲泼尼龙冲击,口服多巴丝肼、普拉克索后患者症状消失,未遗留明显后遗症。结论熟悉无电解质紊乱的渗透性脱髓鞘疾病的典型影像学表现,对早期诊断具有较高价值。
关键词(KeyWords)： 锥体外系;渗透性脱髓鞘;电解质正常;影像学特点;多巴丝肼;普拉克索
基金项目(Foundation):
作者(Author): 郑雪姣,高晓宇,狄政莉,景芸芸,燕玉娥
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